Accepted
at 12:32 p.m. Aug, 07, 2025
by
jaynguyen
Author:
harrisonedwards
Co-authors:
jaynguyen
Type of change:
Other
Rationale for change
Suggest deleting scar card. Bolognia (Fig. 32.5) and Rook (69.12) say JEB gen sev does/may cause scarring. Also, the lesions around the mouth and buttocks (Rook: nose, mouth, neck, trunk, buttocks) are classically "non-healing, crusted erosions containing exuberant granulation tissue", not scarred blister sites.
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Personal Notes
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Missed Questions
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DermPath
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Dermoscopy
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VisualDx
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DermNet
Full Spectrum of Dermatology
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Dermnemonics
Bull-horn: Perioral lesions
Hippie propaganda in back pockets: Buttocks lesions
Hippie propaganda in back pockets: Buttocks lesions
Dermatographix
Junctional Epidermolysis Bullosa (JEB)
- Cowboy with a lasso = Blisters form through the lamina lucida (lamina LASSO-da)
- Little cowboy with bad teeth = Enamel hypoplasia, pitting, and tooth loss in all forms
- Reeses chocolate = Autosomal recessive inheritance
JEB Subtypes
Generalized Severe Form
- Cowboy with a severely damaged outfit = Generalized severe form
- Pet llama with 332 hp = Laminin 332 protein affected
- Damaged hemidesmosome = Absent or rudimentary hemidesmosomes
- Baby cowboy with diapers and crying with a red open mouth = Blisters on buttocks, oral, and perioral regions
- Red earmuffs = Blisters on the pinna of the ears
- Squiggly lines = Hoarse cry due to laryngeal involvement
- Laryngeal links on chain = Laryngeal involvement
- Thumbs up = Blisters heal without scarring
- Clown with red paint around the mouth = Perioral granulation tissue developing after six months
- Baby cowboy with a lung-shaped respiratory vest = Death from respiratory failure
- Cowboy lying on the floor covered in blood and germs = Death from septicemia
Generalized Intermediate Form
- Cowboy with a less damaged outfit = Generalized intermediate form
- Llama with 332 hp = Laminin 332 protein affected
- Pirate with two peg legs = BPAG2 (collagen 17) protein affected
- Bald pirate = Scarring alopecia
- Thin atrophic tissue paper = Lesions heal with atrophic scarring
Junctional EB with Pyloric Atresia
- Baby with a pyloric purse = JEB with pyloric atresia
- Beta-shaped sunglasses = a6B4 integrin protein affected
- Cowboy squeezing a bladder-shaped cup = Ureteral stenosis
- Elf with tiny ears = Rudimentary and malformed ears
- Skull with crossbones on elf’s shirt = Poor prognosis and high mortality rate
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